{"id":4977,"date":"2020-08-31T15:53:29","date_gmt":"2020-08-31T14:53:29","guid":{"rendered":"https:\/\/www.climsom.com\/blog\/?p=4977"},"modified":"2020-09-01T10:42:33","modified_gmt":"2020-09-01T09:42:33","slug":"syndrome-de-rett-comment-soulager-mon-enfant","status":"publish","type":"post","link":"https:\/\/www.climsom.com\/blog\/syndrome-de-rett-comment-soulager-mon-enfant\/","title":{"rendered":"Syndrome de Rett : comment soulager mon enfant ?"},"content":{"rendered":"\n<p>Troubles intellectuelles et motrices, insomnies, handicaps physiques, le Syndrome de Rett est une maladie qui bouleverse le d\u00e9veloppement du syst\u00e8me nerveux central.<br>Si les premiers mois de vie, g\u00e9n\u00e9ralement de la petite fille, semblent normaux, la r\u00e9gression est rapide et seuls les sympt\u00f4mes peuvent \u00eatre soulag\u00e9s.<\/p>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h2 class=\"wp-block-heading\">Syndrome de Rett et troubles du sommeil&nbsp;: comment aider \u00e0 mieux dormir&nbsp;?<\/h2>\n\n\n\n<p>D\u00e8s la premi\u00e8re phase de r\u00e9gression, des <strong>insomnies<\/strong> peuvent accompagner la maladie. Votre enfant n&rsquo;arrive pas \u00e0 s&rsquo;endormir, pleure, et se r\u00e9veille dans la nuit&#8230; <br><br>L&rsquo;apparition d&rsquo;une scoliose importante dans les ann\u00e9es suivantes peut \u00e0 son tour d\u00e9t\u00e9riorer la qualit\u00e9 des nuits en causant des <strong>bouff\u00e9es de chaleur<\/strong> et <strong>sueurs nocturnes<\/strong>.<br>Apr\u00e8s s&rsquo;\u00eatre p\u00e9niblement endormi, ce sont donc de nouveaux \u00e9l\u00e9ments qui peuvent perturber le sommeil de votre enfant et le r\u00e9veiller en pleine nuit.<br><br>Ces troubles du sommeil causent une grande fatigue pour la journ\u00e9e qui suit, ce qui n&rsquo;am\u00e9liore en rien les autres sympt\u00f4mes du Syndrome de Rett.<\/p>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h3 class=\"wp-block-heading\">R\u00e9duire les insomnies, bouff\u00e9es de chaleur et su\u00e9es nocturnes sans danger<\/h3>\n\n\n\n<p>D&rsquo;apr\u00e8s une <a href=\"https:\/\/www.climsom.com\/fra\/etude-centre-sommeil-leger-2011.php?bcklink=1\" target=\"_blank\" rel=\"noreferrer noopener\">\u00e9tude<\/a> men\u00e9e par le Professeur Damien L\u00e9ger, du Centre du Sommeil et de la Vigilance de l&rsquo;H\u00f4tel-Dieu, <strong>l&rsquo;apport de fra\u00eecheur durant la nuit peut nettement am\u00e9liorer la qualit\u00e9 du sommeil.<\/strong><br>Dans ce cadre, il a \u00e9t\u00e9 d\u00e9couvert que le <a href=\"https:\/\/www.climsom.com\/fra\/sur-matelas-rafraichissant-chauffant-jambes-lourdes.php?codeoffer=CS&amp;bcklink=1\" target=\"_blank\" rel=\"noreferrer noopener\">surmatelas Climsom Personal<\/a> influait positivement le sommeil \u00e0 hauteur de <strong>58%<\/strong> !<br><\/p>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-large\"><img loading=\"lazy\" decoding=\"async\" width=\"450\" height=\"300\" src=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/Climsom_Surmatelas_Personal_lit_femme_allongee_50-450x300.jpg\" alt=\"\" class=\"wp-image-4988\" srcset=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/Climsom_Surmatelas_Personal_lit_femme_allongee_50-450x300.jpg 450w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/Climsom_Surmatelas_Personal_lit_femme_allongee_50-300x200.jpg 300w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/Climsom_Surmatelas_Personal_lit_femme_allongee_50-768x512.jpg 768w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/Climsom_Surmatelas_Personal_lit_femme_allongee_50.jpg 1000w\" sizes=\"auto, (max-width: 450px) 100vw, 450px\" \/><\/figure><\/div>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<p>Surmatelas climatis\u00e9, le Climsom Personal permet de contr\u00f4ler la temp\u00e9rature du lit.<br>Lors de l&rsquo;endormissement, la temp\u00e9rature corporelle perd 1\u00b0C. Ainsi, en s\u00e9lectionnant une temp\u00e9rature fra\u00eeche, nous aidons le corps \u00e0 perdre ce degr\u00e9 et <strong>acc\u00e9l\u00e9rons l&rsquo;endormissement<\/strong> !<br><br>Aussi, <strong>dormir dans un lit frais limite le risque de bouff\u00e9es de chaleur nocturnes et de sudation excessive<\/strong>. Nous diminuons donc le risque de r\u00e9veils et d&rsquo;agitations la nuit !<br><br>Parmi les bienfaits du surmatelas climatis\u00e9 Climsom, nous relevons une <strong>diminution de la somnolence en journ\u00e9e de 33%<\/strong>. Ce param\u00e8tre tr\u00e8s important dans le d\u00e9veloppement chez l&rsquo;enfant l&rsquo;est d&rsquo;autant plus en cas de Syndrome de Rett !<\/p>\n\n\n\n<div style=\"height:40px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h3 class=\"wp-block-heading\">Le froid pour soulager les douleurs la nuit<\/h3>\n\n\n\n<p>Le froid est pourvu de propri\u00e9t\u00e9s <strong>antalgiques<\/strong> et <strong>anti-inflammatoires<\/strong>. Le r\u00e9flexe petits pois surgel\u00e9s pour calmer la douleur, nous le connaissons tous&nbsp;!<br><br>Si l&rsquo;expression des sentiments ou de la douleur n&rsquo;est pas \u00e9vidente chez un enfant atteint du Syndrome de Rett, nous savons que la fra\u00eecheur peut, elle, soulager. <br>En cas de scoliose grave et de douleurs, le surmatelas Climsom les soulage alors notamment au moment du coucher et limite les douleurs nocturnes. Attention, soulager les douleurs ne dispense pas un suivi aupr\u00e8s de professionnels de sant\u00e9 comme un kin\u00e9sith\u00e9rapeute. <br><br><br>Par ailleurs, pr\u00e9f\u00e9rer un surmatelas climatis\u00e9 plut\u00f4t qu&rsquo;une climatisation limite les risques li\u00e9s aux troubles respiratoires comme l&rsquo;asthme.<\/p>\n\n\n\n<div style=\"height:30px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<div class=\"wp-block-media-text alignwide is-stacked-on-mobile\" style=\"grid-template-columns:26% auto\"><figure class=\"wp-block-media-text__media\"><img loading=\"lazy\" decoding=\"async\" width=\"339\" height=\"300\" src=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/04\/Climsom_themocontroleur_surmatelas_telecommande-339x300.jpg\" alt=\"\" class=\"wp-image-3801\" srcset=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/04\/Climsom_themocontroleur_surmatelas_telecommande-339x300.jpg 339w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/04\/Climsom_themocontroleur_surmatelas_telecommande-300x265.jpg 300w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/04\/Climsom_themocontroleur_surmatelas_telecommande-768x679.jpg 768w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/04\/Climsom_themocontroleur_surmatelas_telecommande-370x327.jpg 370w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/04\/Climsom_themocontroleur_surmatelas_telecommande.jpg 1000w\" sizes=\"auto, (max-width: 339px) 100vw, 339px\" \/><\/figure><div class=\"wp-block-media-text__content\">\n<p style=\"font-size:15px\">Le surmatelas Climsom Personal s&rsquo;installe simplement entre le matelas et le drap housse. Reli\u00e9 gr\u00e2ce \u00e0 un flexible, le thermocontr\u00f4leur est lui pos\u00e9 au sol, g\u00e9n\u00e9ralement au pied du lit.<br>Ce thermocontr\u00f4leur est \u00e9galement tr\u00e8s facile d&rsquo;utilisation : il suffit de s\u00e9lectionner la temp\u00e9rature voulue sur l&rsquo;\u00e9cran ou gr\u00e2ce \u00e0 la t\u00e9l\u00e9commande, et de la valider !<br>Des fonctions compl\u00e9mentaires vous permettent de programmer le d\u00e9marrage ou l&rsquo;arr\u00eat de l&rsquo;appareil par exemple.<\/p>\n<\/div><\/div>\n\n\n\n<div style=\"height:50px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h3 class=\"wp-block-heading\">T\u00e9moignage<\/h3>\n\n\n\n<p class=\"has-background\" style=\"background-color:#d7d7d7\">\u00ab\u00a0<em>Les tutrices et moi avons procur\u00e9 un surmatelas\u00a0Climsom \u00e0 ma belle fille polyhandicap\u00e9e ( Syndrome de Rett \/ troubles autistiques) et qui me semble <strong>hypersensible \u00e0 la chaleur<\/strong>.\u00a0<br>J&rsquo;avoue avoir \u00e9t\u00e9 \u00ab\u00a0bluff\u00e9\u00a0\u00bb par le r\u00e9sultat.<strong> Elle semble beaucoup mieux dormir<\/strong> m\u00eame en temps de chaleur mod\u00e9r\u00e9e et fait plus facilement des siestes l&rsquo;apr\u00e8s-midi.<br>Par ailleurs nous nous inqui\u00e9tons des risques d&rsquo;asthme ou m\u00eame de qualit\u00e9\u00a0d&rsquo;air avec une climatisation traditionnelle (sans compter le co\u00fbt de la d\u00e9pense \u00e9nerg\u00e9tique et la pollution induite&#8230;).<\/em>\u00ab\u00a0<\/p>\n\n\n\n<div style=\"height:40px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<div class=\"wp-block-columns is-layout-flex wp-container-core-columns-is-layout-28f84493 wp-block-columns-is-layout-flex\">\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\">\n<h3 class=\"wp-block-heading\">Contenu du pack<\/h3>\n\n\n\n<ul class=\"wp-block-list\"><li>1 surmatelas une place : 70 x 190 cm<\/li><li>1 thermocontroleur pour ma\u00eetriser la temp\u00e9rature<\/li><li>1 flexible de 1m pour relier le thermocontr\u00f4leur au surmatelas<\/li><li>1 t\u00e9l\u00e9commande (et ses piles) pour contr\u00f4ler l&rsquo;appareil \u00e0 distance<\/li><li>Une notice d&rsquo;utilisation compl\u00e8te<\/li><\/ul>\n<\/div>\n\n\n\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\">\n<h3 class=\"wp-block-heading\">Avantages Climsom<\/h3>\n\n\n\n<ol class=\"wp-block-list\"><li><strong>Garantie 30 jours satisfait ou rembours\u00e9<\/strong> pour tester le pack surmatelas climatis\u00e9 sans prendre de risque<\/li><li>Livraison gratuite<\/li><li>Un service client disponible pour vous r\u00e9pondre personnellement du lundi au vendredi.<br><strong>TEL :<\/strong> 02 85 52 44 74<br><strong>MAIL :<\/strong> <a href=\"mailto:contact@climsom.com\">contact@climsom.com<\/a><\/li><\/ol>\n\n\n\n<p><\/p>\n<\/div>\n<\/div>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-large is-resized\"><img loading=\"lazy\" decoding=\"async\" src=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-650x214.png\" alt=\"\" class=\"wp-image-3075\" width=\"441\" height=\"144\" srcset=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-650x214.png 650w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-300x99.png 300w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-768x253.png 768w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-370x122.png 370w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1.png 905w\" sizes=\"auto, (max-width: 441px) 100vw, 441px\" \/><\/figure><\/div>\n\n\n\n<div class=\"wp-block-buttons aligncenter is-layout-flex wp-block-buttons-is-layout-flex\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link has-vivid-cyan-blue-to-vivid-purple-gradient-background has-background\" href=\"https:\/\/www.climsom.com\/fra\/sur-matelas-rafraichissant-chauffant-jambes-lourdes.php?codeoffer=CS&amp;bcklink=1\" target=\"_blank\" rel=\"noreferrer noopener\">J&rsquo;aide mon enfant atteint du Syndrome de Rett \u00e0 mieux dormir<\/a><\/div>\n<\/div>\n\n\n\n<div style=\"height:30px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h2 class=\"wp-block-heading\">Qu\u2019est-ce que le Syndrome de Rett&nbsp;?<\/h2>\n\n\n\n<p>Le Syndrome de Rett est une <strong>maladie g\u00e9n\u00e9tique<\/strong> due \u00e0 une mutation du g\u00e8ne MECP2 situ\u00e9 sur le chromosome X. Il touche tr\u00e8s majoritairement les filles \u00e0 partir de 6 mois, seuls des cas isol\u00e9s ont \u00e9t\u00e9 relev\u00e9s chez des gar\u00e7ons.<br><br>Il se caract\u00e9rise par des d\u00e9ficiences intellectuelles et motrices prononc\u00e9es chez l\u2019enfant qui apparaissent avec le temps.<\/p>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h3 class=\"wp-block-heading\">Vivre avec le Syndrome de Rett<\/h3>\n\n\n\n<p>Dans sa forme dite typique ou classique, la maladie connait 4 phases principales.<br><br><strong>De 0 \u00e0 1 ans<\/strong>, le d\u00e9veloppement de l\u2019enfant est normal ou quasi-normal&nbsp;: la marche peut s\u2019acqu\u00e9rir et le p\u00e9rim\u00e8tre cr\u00e2nien (taille du tour de t\u00eate) est normal. C\u2019est une <strong>phase silencieuse<\/strong>.<br><br><br><strong>De 1 \u00e0 4 ans, <\/strong>l\u2019enfant entre dans une phase de <strong>r\u00e9gression rapide<\/strong> pouvant faire penser \u00e0 de l\u2019autisme.<br>C\u2019est durant cette phase qu\u2019apparaissent les premiers troubles du comportement&nbsp;: retrait social, pleurs, troubles moteurs (d\u00e9ficiences et apparition de mouvements r\u00e9p\u00e9titifs).<br><br>Durant cette phase de r\u00e9gression, retard psychomoteur avanc\u00e9,<strong> insomnies<\/strong> et convulsions sont \u00e9galement constat\u00e9s. Le langage quant \u00e0 lui ne s\u2019acquiert pas et l\u2019\u00e9quilibre \u00e0 la marche est tr\u00e8s limit\u00e9 voire non acquis.<\/p>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-large is-resized\"><img loading=\"lazy\" decoding=\"async\" src=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/syndrome-de-rett-fillette-450x300.jpg\" alt=\"Le syndrome de Rett touche tr\u00e8s majoritairement les petites filles\" class=\"wp-image-5008\" width=\"349\" height=\"233\" srcset=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/syndrome-de-rett-fillette-450x300.jpg 450w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/syndrome-de-rett-fillette-300x200.jpg 300w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/syndrome-de-rett-fillette-768x512.jpg 768w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/08\/syndrome-de-rett-fillette.jpg 886w\" sizes=\"auto, (max-width: 349px) 100vw, 349px\" \/><\/figure><\/div>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<p><strong>De 2 \u00e0 10 ans<\/strong> selon l\u2019\u00e2ge de survenue de la r\u00e9gression rapide, <strong>le syndrome se stabilise<\/strong>. Au cours de cette p\u00e9riode, l\u2019enfant sera sujet \u00e0 une d\u00e9ficience intellectuelle, des convulsions ou encore des troubles de la respiration.<br>Les troubles autistiques quant \u00e0 eux ont tendance \u00e0 reculer, de m\u00eame que le retrait social.<br><br><br><strong>A partir de 10 ans<\/strong> selon la dur\u00e9e de la p\u00e9riode de stabilisation, le volume musculaire diminue de fa\u00e7on nette entra\u00eenant une perte de motricit\u00e9, des raideurs et par cons\u00e9quent un handicap moteur important.<br><br>Cette perte du volume musculaire est \u00e9galement \u00e0 l\u2019origine d\u2019une <strong>scoliose<\/strong> importante, pouvant elle-m\u00eame engendrer des <strong>bouff\u00e9es de chaleur<\/strong> et <strong>sueurs nocturnes <\/strong>(troubles trophiques et vasomoteurs).<br>L\u2019ensemble de ces bouleversements est dans la grande majorit\u00e9 des cas accompagn\u00e9 d\u2019<strong>\u00e9pilepsie<\/strong>.<br><br><br>A ce jour, aucun traitement n\u2019existe pour gu\u00e9rir du Syndrome de Rett. Seule une prise en charge des sympt\u00f4mes est possible.<br><br>Cette maladie touche 25 \u00e0 40 naissances par an en France. En cas de besoin, l&rsquo;<a href=\"https:\/\/afsr.fr\/\" target=\"_blank\" rel=\"noreferrer noopener\">Association Fran\u00e7aise du Syndrome de Rett<\/a> vous guide et vous accompagne dans vos d\u00e9marches.<\/p>\n\n\n\n<div style=\"height:30px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<div class=\"wp-block-image\"><figure class=\"aligncenter size-large is-resized\"><img loading=\"lazy\" decoding=\"async\" src=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-650x214.png\" alt=\"\" class=\"wp-image-3075\" width=\"441\" height=\"144\" srcset=\"https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-650x214.png 650w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-300x99.png 300w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-768x253.png 768w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1-370x122.png 370w, https:\/\/www.climsom.com\/blog\/wp-content\/uploads\/2020\/03\/Fleche-call-to-action-noir-1.png 905w\" sizes=\"auto, (max-width: 441px) 100vw, 441px\" \/><\/figure><\/div>\n\n\n\n<div class=\"wp-block-buttons aligncenter is-layout-flex wp-block-buttons-is-layout-flex\">\n<div class=\"wp-block-button\"><a class=\"wp-block-button__link has-vivid-cyan-blue-to-vivid-purple-gradient-background has-background\" href=\"https:\/\/www.climsom.com\/fra\/sur-matelas-rafraichissant-chauffant-jambes-lourdes.php?codeoffer=CS&amp;bcklink=1\" target=\"_blank\" rel=\"noreferrer noopener\">Am\u00e9liorer le sommeil en cas de Syndrome de Rett<\/a><\/div>\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>Troubles moteurs et intellectuels, le Syndrome de Rett est une maladie qui touche principalement les petites filles. Lourde au quotidien, d\u00e9couvrez comment soulager certains sympt\u00f4mes de la maladie.<\/p>\n","protected":false},"author":1,"featured_media":4980,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[10,8],"tags":[145,130],"class_list":["post-4977","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-sante","category-sommeil","tag-syndrome-de-rett","tag-troubles-du-sommeil"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Syndrome de Rett : comment soulager mon enfant ? - Climsom \u2013 L\u2019innovation bien-\u00eatre<\/title>\n<meta name=\"description\" content=\"Votre enfant est atteint du Syndrome de Rett ? 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